Less common disorders:X

佚名

DISEASE AND CAUSES PATHOPHYSIOLOGY SIGNS AND SYMPTOMS
X-linked infantile hypogammaglobulinemia
  • Congenital disorder
Deficiency or absence of B cells leads to defective immune response and depressed production of all five immunoglobulin types. Recurrent infections starts at about age 6 months:

  • Otitis media, pneumonia, dermatitis, bronchitis, meningitis, conjunctivitis, abnormal dental caries, and polyarthritis

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